Box 1.

Uncommon manifestations in Behçet’s disease

  • Cardiac – coronary vasculitis, pericarditis, myocarditis, endocarditis, coronary aneurysms, valvular disease and arrhythmias

  • Pulmonary – pulmonary opacities, haemorrhage, vasculitis, pleural effusions, pulmonary aneurysms, pulmonary hypertension and fibrosing mediastinitis

  • Renal – mild renal impairment, glomerulonephritis, interstitial nephritis, renal artery aneurysm and amyloidosis

  • Other associations – MAGIC (mouth and genital ulcers with inflamed cartilage) represents features of relapsing chondritis and mucosal ulcers

  • Sweet’s syndrome – fever, nodular rashes, and mouth and genital ulcers