Table 1.

Causes of sudden cardiac death in the young (autopsy-proven)

StudyCountryNAge rangeIncidence (n/100,000/year)Ath CAD (%)CAA (%)Myocarditis (%)HCM (%)ARVC (%)Structurally normal heart (%)Other (%)
Winkel et al 23Denmark3141–351.913170.654330
Thiene et al 4Italy6501–3511851410101726
Bagnall et al 24Australia/New Zealand4901–351.3247161340
Finocchiaro et al 25UK258a7–351.4627.411.647.624
Maron et al 26USA868a14–234.4186.5355328
Wisten et al 27Sweden552 b1–351.315114543130
  • aYoung competitive athletes; b393 autopsy-proven. ARVC = arrhythmogenic right ventricular cardiomyopathy; Ath CAD = atherosclerotic coronary artery disease; CAA = coronary artery anomaly; HCM = hypertrophic cardiomyopathy