Criterion | Description |
---|---|
Mandatory criterion | Purpura or petechiae with lower limb predominance |
Minimum one out of four criteria | 1. Diffuse abdominal pain with acute onset
2. Histopathology showing leukocytoclastic vasculitis or proliferative glomerulonephritis, with predominant IgA deposits 3. Arthritis or arthralgia of acute onset 4. Renal involvement in the form of proteinuria or haematuria |
EULAR = European League Against Rheumatism; Ig, Immunoglobulin; PRES = Paediatric Rheumatology European Society; PRINTO = Paediatric Rheumatology INternational Trials Organisation.