Clinical type of amyloidosis | Amyloid fibril protein | Precursor substance |
---|---|---|
Primary (immunnocytodyscrasia) | AL (amyloid L chain) | Monoclonal immunoglobulin light chain |
Secondary (chronic active disease) eg rheumatoid arthritis, osteomyelitis | AA (amyloid A) | Serum amyloid A protein (SAA) |
Haemodialysis associated | β2 – macroglobulin | |
Heredofamilial (commonly affected kidney), rare |