Cardiac involvement in patients with amyloidosis is common. It produces significant clinical
symptoms in about 40% of patients with AL amyloidosis. A significant proportion of patients …

OBJECTIVE: To determine whether patients with myocardial amyloidosis due either to AL (primary)
amyloid or familial amyloid have distinguishing echocardiographic or …

BACKGROUND: Heart transplantation (TX) for cardiac amyloidosis is uncommon because
of concern about progression of amyloid in other organs and the possibility of amyloid …

Objectives. This study sought to determine the spectrum of electrophysiologic abnormalities
found in patients with cardiac involvement due to AL (primary) amyloidosis and to evaluate …

Aims Heart failure chiefly affects the elderly, with frequent emergency admissions.
Telemonitoring can identify worsening heart failure but previous randomized trials have enrolled …

Cardiac sarcoidosis is an underdiagnosed disease that may be present in as many as 25%
of patients with systemic sarcoidosis. Although most commonly recognized in patients with …

Primary (AL) amyloidosis is a multisystem disease caused by plasma cell dyscrasia and
characterized by the extracellular deposition of immunoglobulin light chains within various …

Background. Familial amyloidosis (FAP) is characterized by the progression of neurologic
and cardiac impairment ultimately leading to death within 7 to 15 years after the onset of the …

This study was designed to characterize the geometry and function of the right ventricle and
its prognostic significance in patients with primary (AL) cardiac amyloidosis. AL amyloidosis …

The fibrils in AL and AA amyloidosis, although similar in appearance, have different
biochemical composition and staining characteristics. Whereas electrocardiographic and …